Abstract: Kartagener's syndrome (KS) is a rare hereditary disease which is also known as Kartagener Afzelius syndrome. It is caused by mutations in many different genes that are inherited in an autosomal recessive manner5. It is a subset of Primary Ciliary Defect (PCD), formerly known as immotile cilia syndrome. The clinical triad of KS includes situs inversus, sinusitis and bronchiectasis8. Usually diagnosed with history, physical examination, laboratory and radiological investigations. Management of KS is as per the presentation of the symptoms. The recently used trend of management is the airway clearance therapy or pulmonary hygiene in order to maintain a patent airway.
Keywords: Kartagener syndrome(KS), Primary Ciliary Defect (PCD), Situs Inversus (SI), Bronchiectasis, Sinusitis.
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